New Guidelines for Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis

Idiopathic pulmonary fibrosis (IPF) is the most common and fatal idiopathic interstitial pneumonia characterized by chronic progressive of indeterminate etiology. In 2018, American Thoracic Society, European Respiratory Japanese Latin Society published joint clinical practice guidelines for IPF. The require exclusion known causes lung disease identification a radiological and/or pathologic pattern usual (UIP). diagnosis IPF multidisciplinary process, involving pulmonologists, radiologists, pathologists and, if necessary, experts in other medical fields. 2022 revisit clarify pathological features UIP. addition, recommendations regarding transbronchial cryobiopsy, antacid medication, antireflux surgery are revised or established based on up-to-date evidence guidelines. new also encompass definition treatment (PPF). PPF comprises diverse fibrotic diseases than IPF, which progress despite standard treatment. symptoms, physiologic evidence, radiologic progression. use nintedanib was suggested patients with who unresponsive to This review introduces discusses international